Abstract
Malignant tumors of mesenchymal tissue (sarcomas) originating from the dermis and subcutis are discussed in this chapter. In addition, some sarcomas locate in deeper soft tissue (subfascial sarcomas), and the skin may be involved secondarily by the extension of the tumor. These sarcomas are mainly diagnosed and treated by orthopedic surgeons. Sarcomas are classified according to the cell of origin. All cutaneous sarcomas of vascular, fibrous, fatty tissue, nerve sheath, and smooth muscle origin are rare. Cutaneous sarcomas with vascular differentiation are localized on relatively superficial parts of the skin and have typical clinical features, but most other sarcomas present with nonspecific nodules or poorly defined deep masses that may only be diagnosed by histopathologic examination. Cutaneous sarcomas are generally not transformed from benign skin or soft tissue tumors. While some of these cutaneous sarcomas are low grade and have a better prognosis than their counterparts in deeper tissue, many have an aggressive course with a potential for systemic metastasis. Early diagnosis is essential to decrease the morbidity and mortality of these tumors.
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Baykal, C., Yazganoğlu, K.D. (2014). Cutaneous Sarcomas. In: Clinical Atlas of Skin Tumors. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-40938-7_13
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DOI: https://doi.org/10.1007/978-3-642-40938-7_13
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