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Ocular Adnexal Lymphoma: Staging and Treatment

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Ocular and Adnexal Lymphoma

Part of the book series: Essentials in Ophthalmology ((ESSENTIALS))

Abstract

A definitive diagnosis of ocular adnexal lymphoma (OAL) is based upon biopsy as benign conditions including reactive lymphoid hyperplasia cannot be differentiated based on clinical grounds alone. Once the diagnosis has been established, OAL is classified and staging is performed. OAL can coexist with lymphoma in other systemic sites in 15–25 % of cases. For this reason, a multidisciplinary approach is necessary and includes a thorough systemic evaluation and referral to an experienced medical oncologist.

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Authors and Affiliations

  1. Department of Ophthalmic Oncology, Cole Eye Institute, Cleveland Clinic Foundation, 9500 Euclid Ave R35, Cleveland, OH, 44195, USA

    Mary E. Aronow MD & Arun D. Singh MD

  2. Huntsman Cancer Institute, University of Utah, 1950 Circle of Hope, Salt Lake City, UT, 84112, USA

    John W. Sweetenham MD

Authors
  1. Mary E. Aronow MD
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  2. Arun D. Singh MD
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  3. John W. Sweetenham MD
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Corresponding author

Correspondence to John W. Sweetenham MD .

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Editors and Affiliations

  1. Dept. of Ophthalmic Oncology, Cole Eye Institute Cleveland Clinic Foundation, Cleveland, Ohio, USA

    Arun D. Singh

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Aronow, M.E., Singh, A.D., Sweetenham, J.W. (2014). Ocular Adnexal Lymphoma: Staging and Treatment. In: Singh, A. (eds) Ocular and Adnexal Lymphoma. Essentials in Ophthalmology. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-38499-8_7

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  • DOI: https://doi.org/10.1007/978-3-642-38499-8_7

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  • Online ISBN: 978-3-642-38499-8

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