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Klinische Manifestation der Autoimmunpankreatitis

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Erkrankungen des Pankreas

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Zusammenfassung

Die Klinik der Autoimmunpankreatitis (AIP) ist äußerst variabel, wodurch die Diagnosestellung erschwert wird. Als Leitsymptome gelten ein Verschlussikterus und mittelgradige abdominelle Schmerzen in Verbindung mit einer fokalen oder diffusen Pankreasvergrößerung. Da mittels abdomineller Schnittbildgebung mitunter fokale Raumforderungen imponieren, ist die Differenzialdiagnose zum Pankreaskarzinom von großer Bedeutung, weil sich dadurch eine vollkommen andere Therapiestrategie ergibt. Aufgrund der sehr ähnlichen klinischen Manifestation sollten die AIP-Subtypen 1 und 2 nur mittels histologischer Diagnose durch einen erfahrenen Pankreaspathologen erfolgen. Beide Subtypen sind gekennzeichnet durch ein außerordentlich gutes Ansprechen auf eine Kortikosteroidtherapie.

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Authors and Affiliations

  1. Klinik für Allgemein-, Viszeral- und Transplantationschirurgie, Universitätsklinikum Heidelberg, Im Neuenheimer Feld 110, 69120, Heidelberg, Deutschland

    Stefan Fritz & Jens Werner

  2. Heidelberg, Deutschland

    Jens Werner

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  1. Stefan Fritz
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  2. Jens Werner
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Corresponding author

Correspondence to Stefan Fritz .

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Editors and Affiliations

  1. Abt. Allgemeine- und Visceralchirurgie, Universitätsklinikum Ulm, Germany

    Hans G. Beger

  2. Klinik für Allgemein-, Viszeral- und Transplantationschirurgie, Universitätsklinikum Heidelberg, Germany

    Markus W. Büchler

  3. Allgemein-, Viszeral- und Gefäßchirurgie, Universitätsklinikum Halle, Sachsen-Anhalt, Germany

    Henning Dralle

  4. Klinik und Poliklinik für Innere Medizin, Universitätsmedizin Greifswald, Germany

    Markus M. Lerch

  5. und Hepatologie (KGHI), Universitätsklinikum Magdeburg, Germany

    Peter Malfertheiner

  6. FB Gastroenterologie und Hepatologie, Universitätsklinikum Leipzig, Sachsen, Germany

    Joachim Mössner

  7. ehemals Klinikum der Stadt Ludwigshafen gGmbH, Rheinland-Pfalz, Germany

    Jürgen F. Riemann

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© 2013 Springer-Verlag Berlin Heidelberg

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Fritz, S., Werner, J. (2013). Klinische Manifestation der Autoimmunpankreatitis. In: Beger, H., et al. Erkrankungen des Pankreas. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-37964-2_30

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  • DOI: https://doi.org/10.1007/978-3-642-37964-2_30

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  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-642-37963-5

  • Online ISBN: 978-3-642-37964-2

  • eBook Packages: Medicine (German Language)

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