Abstract
Pediatric diffuse parenchymal lung diseases comprise a rare and heterogeneous group of chronic lung disorders characterized clinically by dyspnea, tachypnea, crackles, and hypoxemia and are associated with significant morbidity and mortality. While often equated with interstitial lung disease, involvement of the alveoli, airways, blood vessels, lymphatic channels, and pleural spaces in addition to the interstitium is in fact common. Advances in imaging, improved thoracoscopic lung biopsy techniques, and a revised classification system by the Children’s Interstitial Lung Disease (chILD) Research Cooperative have improved understanding of these disorders. Chest radiography (CXR) is the first-line imaging modality. High-resolution computed tomography (HRCT) is preferred, helping to make the diagnosis or differential diagnosis and guide further diagnostic testing.
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© 2014 Springer-Verlag Berlin Heidelberg
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Zucker, E.J., Lee, E.Y. (2014). Pediatric Diffuse Lung Disease. In: Kim, IO. (eds) Radiology Illustrated: Pediatric Radiology. Radiology Illustrated. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-35573-8_15
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DOI: https://doi.org/10.1007/978-3-642-35573-8_15
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