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Sklerodermie und Sharp-Syndrom

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Pädiatrische Rheumatologie

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Zusammenfassung

Das Wort »scleroderma« bedeutet harte Haut. Die Erkrankung Sklerodermie hat jedoch wesentlich mehr Facetten als nur die Verhärtung der Haut. Alle Formen der Sklerodermie sind im Kindesalter selten. Die häufigste Form im Kindesalter ist die lokalisierte Sklerodermie (LS). Sie unterscheidet sich von der systemischen Sklerodemie (SSc) dadurch, dass sie sich meistens nur auf die Haut und das subkutane Gewebe beschränkt, aber ungefähr 10% der Patienten haben auch eine extrakutane Beteiligung.

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Authors and Affiliations

  1. Kompetenz-Zentrum für Uveiits und Sklerodermie im Kindes- und Jugendalter, Hamburger Zentrum für Kinder- und Jugendrheumatologie An der Schön Klinik Hamburg Eilbek, Dehnhaide 120, 22081, Hamburg

    Dr.med. I. Foeldvari

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  1. Klinik für Kinder- und Jugendmedizin, RWTH Aachen, Aachen

    Norbert Wagner

  2. Pädiatrisches Zentrum, Klinikum Stuttgart, Stuttgart

    Günther Dannecker (Ehem. Ärztlicher Direktor am Olgahospital) (Ehem. Ärztlicher Direktor am Olgahospital)

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Foeldvari, I. (2014). Sklerodermie und Sharp-Syndrom. In: Wagner, N., Dannecker, G. (eds) Pädiatrische Rheumatologie. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-34728-3_8

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