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A Life-threatening Cardiomyopathy following Port-a-Cath Infection under Immune Tolerance Therapy

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Abstract

For elimination of inhibitors against factor VIII immune tolerance therapy (Bonnor Malmö-protocol) is Mainly used. It requires intravenous injections twice daily up to several Months — while in early infancy antibodies Mostly appear within the first 36 days of treatment [6]. Therefore, in patients with inhibitors or on prophylactic treatment, Port insertion is increasingly recommended (Fig. 1). We describe a particularly complicated case.

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© 2003 Springer-Verlag Berlin Heidelberg

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Wiegand, G., Rauch, R., Effenberger, W., Brackmann, HH., Hofbeck, M. (2003). A Life-threatening Cardiomyopathy following Port-a-Cath Infection under Immune Tolerance Therapy. In: Scharrer, I., Schramm, W. (eds) 32nd Hemophilia Symposium. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-18150-4_24

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  • DOI: https://doi.org/10.1007/978-3-642-18150-4_24

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-540-43884-7

  • Online ISBN: 978-3-642-18150-4

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