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Cystic Renal Diseases

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Manual of Pediatric Nephrology

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Abstract

Renal cysts represent a wide spectrum of conditions ranging from simple cysts with little or no clinical significance to severe developmental renal abnormalities and progressive (polycystic) kidney disease or syndromes with multiple organ involvement. This chapter describes the clinical and pathological presentation, diagnostic strategies (including imaging and genetic testing), differential diagnoses, prognosis, and management. A precise diagnosis and (family) history is necessary for prognostic purposes, genetic counselling, and prenatal assessment and decision making. Therapeutic trials have begun for polycystic kidney diseases, but results are so far disappointing.

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Author information

Authors and Affiliations

  1. Division of Pediatric Nephrology, Montreal Children’s Hospital, McGill University, 2300, rue Tupper, Montreal, QC, H3H 1P3, Canada

    Indra Gupta & Martin Bitzan

Authors
  1. Indra Gupta
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  2. Martin Bitzan
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Corresponding author

Correspondence to Indra Gupta .

Editor information

Editors and Affiliations

  1. Ped. Nephrol., St. John's Med. Coll. Hosp. Children's Kidney Care Center, Bangalore, India

    Kishore D. Phadke

  2. Montreal Children's Hospital Division of Nephrology, Montreal, Québec, Canada

    Paul Goodyer

  3. Division of Pediatric Nephrology, McGill University and Montreal Children's Hospital, Montreal, Québec, Canada

    Martin Bitzan

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© 2014 Springer-Verlag Berlin Heidelberg

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Gupta, I., Bitzan, M. (2014). Cystic Renal Diseases. In: Phadke, K., Goodyer, P., Bitzan, M. (eds) Manual of Pediatric Nephrology. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-12483-9_5

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  • DOI: https://doi.org/10.1007/978-3-642-12483-9_5

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  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-642-12482-2

  • Online ISBN: 978-3-642-12483-9

  • eBook Packages: MedicineMedicine (R0)

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