Auszug
Alle cholestatischen Erkrankungen der Leber und der Gallenwege beim Neugeborenen gehören zu den jeweils seltenen Krankheiten in dieser Altersgruppe und bedürfen nur in wenigen Fällen einer unmittelbaren chirurgischen Therapie. Diese ist meistens symptomorientiert und nur selten kurativ, denn diese Patienten repräsentieren die größte Gruppe der Lebertransplantationen im Kindesalter. Trotzdem darf der Stellenwert der chirurgischen Erstbehandlung nicht unterschätzt werden, da diese gerade bel seltenen Erkrankungen für den weiteren Verlauf entscheiden sein kann. Das gift z. B. für die Überlebenszeit mit der eigenen Leber bei der Gallengangatresie oder für einen symptomfreien Langzeitverlauf nach Resektionen von Choledochuszysten.
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Petersen, C. (2009). Erkrankungen der Leber und Gallenwege. In: Kinderchirurgie. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-540-89032-4_35
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