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Choroid Plexus Tumors

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Pediatric CNS Tumors

Part of the book series: Pediatric Oncology ((PEDIATRICO))

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The choroid plexus has the highly specific function of producing cerebrospinal fluid (CSF). It is anatomically localized to the parenchymal/ventricular junction in all four ventricles. The choroid plexus is derived from the specialization of ventricular epithelium along certain segments of the neural tube, and there is a common ontogeny between choroid epithelium and cells of glial origin. This can, and does lead to diagnostic confusion in certain cases. Tumors arising from the choroid plexus can display a benign or malignant phenotype, but conversion to a malignant phenotype is a rare event (Chow et al. 1999; Jeibmann et al. 2007). Guerard was the first to describe a choroid plexus tumor in 1833. The first surgical resection was reported by Bielschowsky and Unger in 1906. Thereafter, both Cushing and Dandy reported their experiences with this unusual tumor (Dandy 1922; Davis and Cushing 1925).

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  1. Departments of Neurological Surgery and Pediatrics Division of Pediatric Neurosurgery, University of California San Francisco, 505 Parnassus Avenue, Rm M779, San Francisco, CA, 94143-0112, USA

    Nalin Gupta

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  1. Nalin Gupta
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Correspondence to Nalin Gupta .

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Editors and Affiliations

  1. Departments of Neurological Surgery and Pediatrics, Division of Pediatric Neurosurgery, University of California San Francisco, 505 Parnassus Avenue, Rm M779, San Francisco, CA, 94143-0112, USA

    Nalin Gupta

  2. Departments of Pediatrics and Neurological Surgery, Division of Hematology and Oncology, University of California San Francisco, 505 Parnassus Avenue, San Francisco, CA, 94143-0106, USA

    Anuradha Banerjee

  3. Departments of Radiation Oncology and Neurological Surgery, Helen Diller Family Comprehensive Cancer Center, University of California San Francisco, 1600 Divisadero Street, San Francisco, CA, 94115-1708, USA

    Daphne Haas-Kogan

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Gupta, N. (2010). Choroid Plexus Tumors. In: Gupta, N., Banerjee, A., Haas-Kogan, D. (eds) Pediatric CNS Tumors. Pediatric Oncology. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-540-87979-4_9

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  • DOI: https://doi.org/10.1007/978-3-540-87979-4_9

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