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Vogt-Koyanagi-Harada Disease

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Intraocular Inflammation

Abstract

Vogt-Koyanagi-Harada disease (VKH) is a granulomatous inflammatory disorder affecting the eyes, auditory system, meninges, and skin. An association with ocular inflammation and poliosis was reported by Vogt in 1906. Harada (1926) and Koyanagi (1929) independently described ocular inflammation associated with cerebrospinal fluid pleocytosis and dermal depigmentation, respectively. Later, the disorders described by Vogt, Koyanagi, and Harada were considered to be the same disease process, which came to be known as VKH.

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Acknowledgments

The authors thank Dr. Izumi Yamamoto and Dr. Shigeaki Ohno for providing the illustrations.

Author information

Authors and Affiliations

  1. Doheny Eye Institute, 1450 San Pablo St., DRVC 211, Los Angeles, CA, 90033, USA

    Satoru Kase MD, PhD & Narsing A. Rao MD

Authors
  1. Satoru Kase MD, PhD
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  2. Narsing A. Rao MD
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Corresponding author

Correspondence to Satoru Kase MD, PhD .

Editor information

Editors and Affiliations

  1. Centre of Ophthalmology, University of Tuebingen, Tuebingen, Germany

    Manfred Zierhut

  2. Biomedical Research Centre, Institute of Ophthalmology, Moorfields Eyes Hospital, Department of Medical Retina, UCL, London, United Kingdom

    Carlos Pavesio

  3. School of Medicine, Department of Ophthalmology, Hokkaido University Graduate, Sapporo, Hokkaido, Japan

    Shigeaki Ohno

  4. University of Belo Horizonte, Belo Horizonte, Brazil

    Fernando Orefice

  5. USC Eye Institute, University of Southern California, Los Angeles, California, USA

    Narsing A. Rao

1 Electronic Supplementary Material

Below is the link to the electronic supplementary material.

Case Report 14

Vogt Koyanagi-Harada (PPT 5861 kb)

Case Report 30

Vogt-Koyanagi Harada disease (PPT 9980 kb)

Case Report 47

Atypical case of Vogt-Koyanagi-Harada (PPT 3338 kb)

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Kase, S., Rao, N.A. (2016). Vogt-Koyanagi-Harada Disease. In: Zierhut, M., Pavesio, C., Ohno, S., Orefice, F., Rao, N. (eds) Intraocular Inflammation. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-540-75387-2_96

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  • DOI: https://doi.org/10.1007/978-3-540-75387-2_96

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-540-75385-8

  • Online ISBN: 978-3-540-75387-2

  • eBook Packages: MedicineMedicine (R0)

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