Abstract
Bietti crystalline dystrophy is a mixed dystrophy characterised by the presence of multiple, small refractive crystals situated in the retina, the choroid, the cornea and the lymphocytes. The disease is bilateral and progressive and results in chorioretinal atrophy of the posterior pole of the ocular fundus. It was first described in 1937 as an association of a retinal and a corneal dystrophy in three patients [1]. The term “crystalline dystrophy” was introduced in 1977 [11].
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References
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Puech, B., De Laey, JJ., Meunier, I. (2014). Bietti Crystalline Corneoretinal Dystrophy. In: Puech, B., De Laey, JJ., Holder, G. (eds) Inherited Chorioretinal Dystrophies. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-540-69466-3_38
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DOI: https://doi.org/10.1007/978-3-540-69466-3_38
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