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Heim- und Langzeitbeatmung bei neuromuskulären Erkrankungen

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NeuroIntensiv

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Ausmaß und Häufigkeit der Beteiligung der Atemmuskulatur ist bei den verschiedenen neuromuskulären Erkrankungen (NME) höchst unterschiedlich [48]. Zwar korreliert das Ausmaß der Atemmuskellähmung meist mit dem Grad der allgemeinen Muskelschwäche und körperlichen Behinderung, jedoch gibt es Ausnahmen: so ist bei der amyotrophen Lateralsklerose (ALS) bei 10% der Patienten bereits früh im Erkrankungsverlauf, nicht selten auch als Erstsymptom eine Schwäche der Atemmuskulatur nachzuweisen. Gleiches gilt für die adulte Form der Glykogenose Typ II (α-Glukosidasemangel, M. Pompe) [52].

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  1. Neurologische Klinik, Krankenhaus Rummelsberg, Rummelsberg 71, 90592, Schwarzenbruck

    PD Dr. M. Winterholler

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  1. Neurologische Klinik, Friedrich-Alexander-Universität Erlangen-Nürnberg, Schwabachanlage 6, 91054, Erlangen

    Stefan Schwab  & Peter Schellinger  & 

  2. Klinik für Anästhesiologie, Klinikum der Johannes Gutenberg-Universität Mainz, Langenbeckstr. 1, 55131, Mainz

    Christian Werner

  3. Neurochirurgische Klinik, Ruprecht-Karls-Universität Heidelberg, Im Neuenheimer Feld 400, 69120, Heidelberg

    Andreas Unterberg  & Werner Hacke  & 

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Winterholler, M. (2008). Heim- und Langzeitbeatmung bei neuromuskulären Erkrankungen. In: Schwab, S., Schellinger, P., Werner, C., Unterberg, A., Hacke, W. (eds) NeuroIntensiv. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-540-68317-9_12

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