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Renal Agenesis, Dysplasia, Hypoplasia and Cystic Diseases of the Kidney

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Book cover Pediatric Uroradiology

Part of the book series: Medical Radiology ((Med Radiol Diagn Imaging))

Abstract

Renal malformations represent the most common manifestation of congenital diseases in childhood. Renal agenesis, dysplasia, hypoplasia and cystic renal diseases are such entities. Causes vary; partially they derive from the complex renal organogenesis, and partially they have genetic and inherited reasons. Furthermore, an acquired disease can be present. Today there is increasing evidence that disturbances of the ciliumcentrosome complex form the pathogenetic base of most or many phenotypically different cystic renal diseases on a cellular level (Guay-Woodford 2006). The knowledge of the individual etiology and development helps to understand the disease process, affects further diagnostic and therapeutic management and helps to properly estimate prognosis of these patients and their families, respectively.

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Authors and Affiliations

  1. Department of Radiology, Division of Pediatric Radiology, University Hospital Graz, Auenbruggerplatz 34, 8036, Graz, Austria

    Professor Michael Riccabona MD

  2. Department of Pediatrics, Division of General Pediatrics, University Hospital Graz, Auenbruggerplatz 30, 8036, Graz, Austria

    Professor Ekkehard Ring MD

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  1. Professor Michael Riccabona MD
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  1. Department of Radiology Head of Division of Pediatric Radiology, University Hospital Medical University Graz, Auenbruggerplatz 34, 8036, Graz, Austria

    Richard Fotter MD (Professor and Chairman) (Professor and Chairman)

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Riccabona, M., Ring, E. (2008). Renal Agenesis, Dysplasia, Hypoplasia and Cystic Diseases of the Kidney. In: Fotter, R. (eds) Pediatric Uroradiology. Medical Radiology. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-540-33005-9_10

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