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Angioimmunoblastic T-Cell Lymphoma

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T-Cell and NK-Cell Lymphomas

Part of the book series: Cancer Treatment and Research ((CTAR,volume 176))

Abstract

Angioimmunoblastic T-cell lymphoma (AITL) is one of the most common types of T-cell lymphoma, representing about 15–20% of cases of peripheral T-cell lymphoma (PTCL). It is characterized by a unique clinical presentation and distinct pathologic and molecular features. Classes of drugs particularly active in AITL are emerging; however, treatment of relapsed and refractory disease remains a challenge. This chapter reviews the epidemiology, clinical presentation, pathogenesis, diagnosis, and treatment of AITL.

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Authors and Affiliations

  1. Hematopathology Service, Memorial Sloan Kettering Cancer Center, New York City, USA

    Mariko Yabe & Ahmet Dogan

  2. Lymphoma Service, Memorial Sloan Kettering Cancer Center, New York City, USA

    Steven M. Horwitz & Alison J. Moskowitz

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  1. Mariko Yabe
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  2. Ahmet Dogan
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  3. Steven M. Horwitz
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  4. Alison J. Moskowitz
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Correspondence to Alison J. Moskowitz .

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  1. Division of Dermatology, Beckman Research Institute, City of Hope National Medical Center, Duarte, CA, USA

    Christiane Querfeld

  2. Department of Hematology and Hematopoietic Cell Transplantation, City of Hope National Medical Center, Duarte, CA, USA

    Jasmine Zain

  3. Department of Hematology and Hematopoietic Cell Transplantation, Beckman Research Institute, City of Hope National Medical Center, Duarte, CA, USA

    Steven T. Rosen

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Yabe, M., Dogan, A., Horwitz, S.M., Moskowitz, A.J. (2019). Angioimmunoblastic T-Cell Lymphoma. In: Querfeld, C., Zain, J., Rosen, S. (eds) T-Cell and NK-Cell Lymphomas. Cancer Treatment and Research, vol 176. Springer, Cham. https://doi.org/10.1007/978-3-319-99716-2_5

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