Abstract
Chronic thromboembolic pulmonary hypertension (CTEPH), representing group 4 of the classification of pulmonary hypertension (PH), is defined as a symptomatic PH with a mean pulmonary arterial pressure (PAm) of at least 25 mmHg and normal pulmonary arterial occlusion pressure (PAOP ≤15 mmHg) with pulmonary perfusion defects persisting after a 3 months episode of adequate anticoagulation [5]. Furthermore, there is a mechanical obstructive component, potentially amenable by surgery and a variable degree of secondary vasculopathy [10].
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Disclosures
CB Wiedenroth has received speaker fees and/or consultant honoraria from Actelion, Bayer AG, BTG, MSD, and Pfizer.
E Mayer has received speaker fees and/or honoraria for consultations from Actelion, Bayer AG, GSK, MSD, and Pfizer.
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Wiedenroth, C.B., Mayer, E. (2019). Pulmonary Hypertension. In: Feldman, D., Mohacsi, P. (eds) Heart Failure. Cardiovascular Medicine. Springer, Cham. https://doi.org/10.1007/978-3-319-98184-0_22
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DOI: https://doi.org/10.1007/978-3-319-98184-0_22
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