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Transplant Considerations in Alagille Syndrome

  • Evelyn Hsu
  • Elizabeth RandEmail author
Chapter

Abstract

Children with Alagille syndrome are often considered for liver transplantation, for a number of indications that include refractory pruritus and end-stage liver disease. It is a well-established therapy with reasonable success. The multi-system nature of this condition dictates a considered approach to liver transplant evaluation and management in order to assure a good outcome.

Keywords

Alagille Pediatric liver transplant Transplant indications and selection Long-term outcomes Surgical complications 

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Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  1. 1.Department of PediatricsUniversity of Washington School of Medicine, Seattle Children’s HospitalSeattleUSA
  2. 2.Department of PediatricsThe University of Pennsylvania School of MedicinePhiladelphiaUSA

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