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Transplant Considerations in Alagille Syndrome

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Alagille Syndrome

Abstract

Children with Alagille syndrome are often considered for liver transplantation, for a number of indications that include refractory pruritus and end-stage liver disease. It is a well-established therapy with reasonable success. The multi-system nature of this condition dictates a considered approach to liver transplant evaluation and management in order to assure a good outcome.

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Author information

Authors and Affiliations

  1. Department of Pediatrics, University of Washington School of Medicine, Seattle Children’s Hospital, Seattle, WA, USA

    Evelyn Hsu

  2. Department of Pediatrics, The University of Pennsylvania School of Medicine, Philadelphia, PA, USA

    Elizabeth Rand

Authors
  1. Evelyn Hsu
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  2. Elizabeth Rand
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Corresponding author

Correspondence to Elizabeth Rand .

Editor information

Editors and Affiliations

  1. Division of Gastroenterology, Hepatology and Nutrition, The Hospital for Sick Children, Toronto, ON, Canada

    Binita M. Kamath

  2. Division of Gastroenterology, Hepatology and Nutrition, Children’s Hospital of Philadelphia, Philadelphia, PA, USA

    Kathleen M. Loomes

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Hsu, E., Rand, E. (2018). Transplant Considerations in Alagille Syndrome. In: Kamath, B., Loomes, K. (eds) Alagille Syndrome. Springer, Cham. https://doi.org/10.1007/978-3-319-94571-2_5

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  • DOI: https://doi.org/10.1007/978-3-319-94571-2_5

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-94570-5

  • Online ISBN: 978-3-319-94571-2

  • eBook Packages: MedicineMedicine (R0)

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