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Systemic Right Ventricle

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Heart Failure in Adult Congenital Heart Disease

Part of the book series: Congenital Heart Disease in Adolescents and Adults ((CHDAA))

Abstract

In the majority of adult congenital heart disease (ACHD) conditions, the patterns of heart failure (HF) closely mirror those seen in acquired disease. However certain conditions present unique physiology—these include those with a right ventricle (RV) in the sub-aortic position (systemic RV). As patients with systemic RVs age, their risk of heart failure significantly increases. There are multiple possible mechanisms that drive ventricular dysfunction, effort intolerance and overt heart failure. Some of these are very specific to the transposition patient such as baffle function and sub-aortic RV physiology. This chapter describes the factors that may contribute to the development of HF and the possible therapeutic options.

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Authors and Affiliations

  1. Royal Brompton Hospital, London, UK

    Lorna Swan

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  1. Lorna Swan
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Editors and Affiliations

  1. Royal Brompton Hospital, London, United Kingdom

    Lorna Swan

  2. ATTIKON University Hospital, Athens University, Athens, Greece

    Alexandra A. Frogoudaki

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Swan, L. (2018). Systemic Right Ventricle. In: Swan, L., Frogoudaki, A. (eds) Heart Failure in Adult Congenital Heart Disease. Congenital Heart Disease in Adolescents and Adults. Springer, Cham. https://doi.org/10.1007/978-3-319-77803-7_7

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  • DOI: https://doi.org/10.1007/978-3-319-77803-7_7

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-77802-0

  • Online ISBN: 978-3-319-77803-7

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