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Temporal Bone Malignancies in Children

  • Elton Lambert
Chapter

Abstract

Temporal bone malignancies in children often present with signs and symptoms often associated with more common pediatric ear symptoms. Ear pain, ear drainage, and hearing loss may be present in these tumors, but when present, signs such as cranial nerve deficits and masses are particularly worrisome. Imaging including CT and MRI is important to determine extent of tumor and to give some clues as to the nature of the mass. Biopsy is often required. Common temporal bone malignancies include rhabdomyosarcoma and Langerhans cell histiocytosis. Osteosarcoma, Ewing’s sarcoma, and malignancies of the lymphoreticular system should also be considered. A combination of chemotherapy, radiation, and surgery forms the treatment plan for these malignancies. Due to the common pathologies encountered in the pediatric population, the role of surgery is usually for biopsy of the lesion or in the treatment of residual tumor after chemotherapy and radiation. Primary surgical therapy is appropriate in some cases.

Keywords

Rhabdomyosarcoma Langerhans histiocytosis Ewing’s sarcoma Osteosarcoma Chondrosarcoma Radiation-associated malignancy Pediatric Temporal bone cancer Acute leukemia Late effects of treatment Chemotherapy 

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Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  1. 1.Pediatric OtolaryngologyTexas Children’s Hospital/Baylor College of MedicineHoustonUSA

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