Abstract
This chapter discusses rare tumors of the temporal bone. While squamous cell carcinoma is the most common tumor to affect the temporal bone, other rare tumors are recognized. These tumor types include endolymphatic sac tumors, giant-cell tumor, and hemangiopericytoma. These tumors have unique characteristics and are individually discussed. Endolymphatic sac tumors and hemangiopericytomas are highly vascular tumors that often require preoperative embolization. Complete surgical excision is treatment of choice but is often difficult to achieve given the anatomy of the temporal bone. Radiotherapy offers reasonable local control in the postoperative setting when residual tumor remains.
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Gidley, P.W. (2018). Unusual Tumors of the Temporal Bone. In: Gidley, P., DeMonte, F. (eds) Temporal Bone Cancer. Springer, Cham. https://doi.org/10.1007/978-3-319-74539-8_11
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