Unusual Tumors of the Middle Ear

  • Paul W. Gidley


Middle ear tumors are more uncommon than ear canal tumors. Often, these tumors present as conductive hearing loss or as chronic otitis media. This chapter reviews the tumors that occur in the middle ear, excepting squamous cell carcinoma. The pathologic nomenclature has evolved over time. Middle ear adenomatous neoplasms, neuroendocrine adenomatous middle ear neoplasm, and carcinoid tumors are grouped under the same heading. Inverting papilloma, Schneiderian papilloma, and Schneiderian carcinoma are considered as a spectrum of a single clinical entity. Middle ear adenocarcinoma, lymphoepithelial-like carcinoma, and aggressive papillary tumor of the middle ear are also discussed.


Middle ear adenomatous neoplasms Neuroendocrine adenomatous middle ear neoplasm Middle ear carcinoid tumor Inverting papilloma Schneiderian papilloma Schneiderian carcinoma Middle ear adenocarcinoma Lymphoepithelial-like carcinoma Aggressive papillary tumor 


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© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  1. 1.Department of Head and Neck SurgeryThe University of Texas M.D. Anderson Cancer CenterHoustonUSA

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