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Erythema Elevatum Diutinum

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Neutrophilic Dermatoses

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Abstract

Erythema elevatum diutinum can be thought of as a rare presentation of chronic cutaneous vasculitis. Although the exact pathogenesis is unknown, it has been associated with a wide range of clinical illnesses including IgA monoclonal gammopathy, myelodysplastic syndrome, rheumatoid arthritis, inflammatory bowel disease, streptococcal infection, and HIV. Lesions typically present as asymptomatic, red-brown papules and nodules symmetrically distributed with a predilection for skin overlying joints, buttocks, and the Achilles tendon. Dapsone is considered first-line treatment.

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Acknowledgements

We thank Omar Sangueza, MD, Professor of Pathology and Dermatology, Wake Forest University School of Medicine for photographs and histology.

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Authors and Affiliations

  1. Department of Dermatology, Weill Cornell Medicine, New York, NY, USA

    Anh N. Tran & Joseph L. Jorizzo

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  1. Anh N. Tran
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  2. Joseph L. Jorizzo
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Editors and Affiliations

  1. Physician (Hon.) of Paris Hospitals, Paris, France

    Daniel Wallach

  2. Pathology Department, APHP Hôpital Saint Louis, Paris, France

    Marie-Dominique Vignon-Pennamen

  3. Dipartimento di Fisiopatologia Medico-Chirurgica e dei Trapianti, Universita’ degli Studi di Milano, Unita’ Operativa di Dermatologia, IRCCS Fondazione Ca’ Granda, Ospedale Maggiore Policlinico, Milano, Italy

    Angelo Valerio Marzano

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Tran, A.N., Jorizzo, J.L. (2018). Erythema Elevatum Diutinum. In: Wallach, D., Vignon-Pennamen, MD., Valerio Marzano, A. (eds) Neutrophilic Dermatoses. Springer, Cham. https://doi.org/10.1007/978-3-319-72649-6_4

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  • DOI: https://doi.org/10.1007/978-3-319-72649-6_4

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