Abstract
Clinical case. Differential diagnosis: SS, Paraneoplastic autonomic ganglionopathy, Systemic lupus erythematosus. Diagnosis: Temporal profile of autonomic symptoms and presence of peripheral polyneuropathy, detection of autoantibodies (ANA, RF, SS-A, and SS-B), salivary gland biopsy. Main autonomic manifestations of SS neuropathy: orthostatic hypotension, sudomotor dysfunction, pupillary signs, gastrointestinal and urinary symptoms. Immunosuppressive therapy. Prognosis.
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Idiaquez, J., Benarroch, E., Nogues, M. (2018). Autonomic Failure in Subacute Sensory Ganglioneuronopathies. In: Idiaquez, J., Benarroch, E., Nogues, M. (eds) Evaluation and Management of Autonomic Disorders. Springer, Cham. https://doi.org/10.1007/978-3-319-72251-1_9
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DOI: https://doi.org/10.1007/978-3-319-72251-1_9
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