Abstract
Clinical case. Differential diagnosis: chronic variant of AAG, Synucleinopathies presenting with PAF phenotype. Diagnosis: Temporal profile of slowly progressive autonomic dysfunction without motor signs. Negative anti-ganglionic acetylcholine receptor antibodies (α3 nAChR). Main autonomic manifestations of PAF: orthostatic hypotension, sudomotor, erectile, bladder dysfunction and constipation. Symptoms management and prognosis.
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Idiaquez, J., Benarroch, E., Nogues, M. (2018). Pure Autonomic Failure. In: Idiaquez, J., Benarroch, E., Nogues, M. (eds) Evaluation and Management of Autonomic Disorders. Springer, Cham. https://doi.org/10.1007/978-3-319-72251-1_6
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DOI: https://doi.org/10.1007/978-3-319-72251-1_6
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