Developmental Defects

  • Giuseppe Micali
  • Anna Elisa Verzì
  • Francesco Lacarrubba


Median raphe cyst clinically appears as a translucent, yellowish, tender nodule that can occur anywhere along the median raphe, located on the ventral side of the male genital area. At dermatoscopy it appears as a homogeneous, white/yellowish structure sometimes associated with a translucent tract (median raphe canal).

Aplasia cutis congenita of the scalp is usually a solitary lesion, located predominately in the vertex and appearing as a noninflammatory, well-demarcated, alopecic patch. Dermatoscopy shows a typical pattern characterized by the presence of a central area of scarring alopecia with no follicular openings and some telangiectatic vessels, and peripheral horizontally and radially oriented hair bulbs (starburst hair follicles pattern).


Developmental defects Congenital malformations Median raphe cyst Median raphe canal Aplasia cutis congenita of the scalp Scarring alopecia Starburst hair follicles pattern 


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© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  • Giuseppe Micali
    • 1
  • Anna Elisa Verzì
    • 1
  • Francesco Lacarrubba
    • 1
  1. 1.Dermatology ClinicUniversity of CataniaCataniaItaly

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