Abstract
Behçet’s disease (BD) is a chronic, relapsing inflammatory multisystem disease of unknown aetiology with the clinical features of mucocutaneous lesions and ocular, vascular, articular, neurologic, gastrointestinal, urogenital, pulmonary, and cardiac involvement [1, 2]. Mucocutaneous lesions are in the clinical presentation and can be considered the hallmarks of the disease. Their knowledge and recognition will permit earlier diagnosis and introduction of treatment with beneficial prognostic results for those affected. In most patients, the diagnosis can be made clinically on the basis of the mucocutaneous symptoms [2]. Since there is no pathognomonic test, multinational data have been recently revised, and International Criteria for Behçet’s Disease (ICBD) have been proposed by an international team as a guide for BD diagnosis and classification [3].
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Alpsoy, E. (2018). Behçet’s Disease. In: Orfanos, C., Zouboulis, C., Assaf, C. (eds) Pigmented Ethnic Skin and Imported Dermatoses. Springer, Cham. https://doi.org/10.1007/978-3-319-69422-1_33
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DOI: https://doi.org/10.1007/978-3-319-69422-1_33
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