Midaortic Syndrome

  • James C. Stanley
  • Jonathan L. Eliason

Case Report

A 15-year-old boy with neurofibromatosis-1 (NF-1) was recognized to have severe hypertension when being screened for a school athletic team. His blood pressure was 225/110 mmHg. His only complaint was lower extremity fatigue with modest physical activity. A continuous systolic bruit that did not vary with respiration was noted in his epigastrium. There was a femoral-radial artery pulse delay. He had palpable pedal pulses, with good capillary fill in his toes. The left border of cardiac dullness was 8 cm to the left of the mid-sternal line with a sustained apical impulse. There were no cardiac murmurs. An electrocardiogram documented mild left ventricular hypertrophy. His chest film revealed a slightly enlarged heart. There was no rib-notching to suggest collateral vessels due to a thoracic aortic coarctation. His basic blood chemistries and urinalysis were normal. Prior to his referral to our hospital he had undergone an attempted percutaneous transluminal angioplasty (PTA)...


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Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  1. 1.Section of Vascular Surgery, Department of SurgeryUniversity of Michigan Cardiovascular Centre, University of Michigan Medical SchoolAnn ArborUSA

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