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Cystic Fibrosis

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Textbook of Pulmonary Rehabilitation

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Abstract

Pulmonary rehabilitation in cystic fibrosis (CF) utilizes the same components as in other respiratory conditions. However, there are some specifics that should be beard in mind. For one, CF is a multi-organ disease with quite variable clinical characteristics and disease burden among individuals. Thus, pulmonary rehabilitation cannot focus solely on the lungs but has to take upper airways, nutritional aspects, the cardiovascular system, liver disease, and the musculoskeletal system into account. Furthermore, people with CF may host various pathogens, which may be (directly or indirectly) transmitted from one person to the other. Infection control measures are, thus, of utmost importance and often interfere with traditional rehabilitation settings such as group sessions. The chapter will focus on aspects of pulmonary rehabilitation which are particularly important in CF. For general information on components of pulmonary rehabilitation, we refer to the respective chapters at the beginning of this book.

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Authors and Affiliations

  1. Epidemiology, Biostatistics and Prevention Institute, University of Zürich, Zurich, Switzerland

    Thomas Radtke & Susi Kriemler

  2. Paediatric Department, Julius-Maximilians University Würzburg, Wuerzburg, Germany

    Helge Hebestreit

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  1. Thomas Radtke
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  2. Susi Kriemler
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  3. Helge Hebestreit
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Editors and Affiliations

  1. Department of Medical and Surgical Sciences, University of Modena, Azienda Ospedaliero Universitaria di Modena Policlinico, Modena, Italy

    Enrico Clini

  2. Alfred Health and Institute for Breathing and Sleep, La Trobe University, Melbourne, Australia

    Anne E. Holland

  3. State University of Londrina, Londrina, Paraná, Brazil

    Fabio Pitta

  4. Department of Rehabilitation Sciences, KU Leuven, Respiratory Division and Rehabilitation, University Hospital Leuven, Leuven, Belgium

    Thierry Troosters

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Radtke, T., Kriemler, S., Hebestreit, H. (2018). Cystic Fibrosis. In: Clini, E., Holland, A., Pitta, F., Troosters, T. (eds) Textbook of Pulmonary Rehabilitation. Springer, Cham. https://doi.org/10.1007/978-3-319-65888-9_27

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  • DOI: https://doi.org/10.1007/978-3-319-65888-9_27

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