• Mohamed Fahmy


Gastroschisis is an old pathology described since 1056; and at the last decade many textbooks exert a lot of effort for the students to learn them how to differentiate between gastroschisis and exampholas; but recently this two entities are well established and easily diagnosed even in the fetus, with the advance of antenatal ultrasound, many centres all over the world now are applying ex utero intrapartum treatment (EXIT) for such cases. Gastroschisis occurred twice as often as omphalocele and is increasing in frequency. Prematurity was commonly seen with gastroschisis, and mortality rate is less in comparison to exampholas, which attributed to low incidence of associated congenital and chromosomal anomalies in the former. The optimal surgical management of gastroschisis remains controversial; options available include primary closure shortly after birth vs staged closure using a silo. The most concerning complication of primary closure is abdominal compartment syndrome, which may lead to ischaemic/necrotic bowel, renal insufficiency and respiratory distress. A staged closure using a spring-loaded silo may prevent the development of abdominal compartment syndrome.


Gastroschisis Antenatal EXIT Prenatal diagnosis Closed gastroschisis 


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Copyright information

© Springer International Publishing AG 2018

Authors and Affiliations

  • Mohamed Fahmy
    • 1
  1. 1.Pediatric SurgeryAl Azher University Pediatric SurgeryCairoEgypt

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