Rare Umbilical Disease

  • Mohamed Fahmy


Congenital navel absence in a viable newborn obviously does not exist. Abnormalities of the connecting stalk (body stalk anomalies) are lethal in utero or impose a therapeutic abortion before any ultrasound picture can document this anomaly, so few cases had been reported. Very serious malformation detected most often on antenatal ultrasound at the end of the first trimester may be associated with absent or attenuated umbilical cord; like Schisis association (neural tube defects with anencephaly, encephalocele and spina bifida cystica), also cases of defective abdominal wall closure with massive visceral hernia, and anencephaly, of course such cases are associated with a higher miscarriage rate.An omphalith is a hard, smooth, pearly white with a firm, dark brown cap calculus of different sizes and shapes found in the umbilicus. Belly button lint is an accumulation of fluffy fibres in the navel cavity. Lint is the common name for visible accumulations of textile fibres and other materials, usually found on and around the umbilicus. Umbilical pilonidal sinus is characterized by penetration of hairs, foreign body reaction and formation of sinus with granulation tissue. Umbilical keloid is a rare disease and could be seen in different forms and at different age group.


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Copyright information

© Springer International Publishing AG 2018

Authors and Affiliations

  • Mohamed Fahmy
    • 1
  1. 1.Pediatric SurgeryAl Azher University Pediatric SurgeryCairoEgypt

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