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Hypertension: Supravalvular Aortic Stenosis

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Disorders of Blood Pressure Regulation

Part of the book series: Updates in Hypertension and Cardiovascular Protection ((UHCP))

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Abstract

Supravalvular aortic stenosis is a rare cause of hypertension. This chapter discusses the incidence, etiology, and pathophysiology of supravalvular aortic stenosis, which is an uncommon form of congenital cardiac disease. Possible clinical presentations, appropriate initial investigations, and follow-up are discussed. Finally, the current literature on the treatment for hypertension in the context of supravalvular aortic stenosis is reviewed.

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Authors and Affiliations

  1. Our Lady’s Hospital for Sick Children, Crumlin, Dublin 12, Ireland

    Daragh Finn M.B., M.R.C.P.I. & Colin J. McMahon MBB.Ch, FRCPI, FAAP, FACC, FAHA

  2. University College Dublin Medical Sciences, Dublin, Ireland

    Daragh Finn M.B., M.R.C.P.I. & Colin J. McMahon MBB.Ch, FRCPI, FAAP, FACC, FAHA

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  1. Daragh Finn M.B., M.R.C.P.I.
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  2. Colin J. McMahon MBB.Ch, FRCPI, FAAP, FACC, FAHA
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Correspondence to Colin J. McMahon MBB.Ch, FRCPI, FAAP, FACC, FAHA .

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Editors and Affiliations

  1. Internal Medicine, American University of Beirut Medical Center, Beirut, Lebanon

    Adel E. Berbari

  2. Emeritus Professor of Medicine, University of Milano-Bicocca, Monza, Italy

    Giuseppe Mancia

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Finn, D., McMahon, C.J. (2018). Hypertension: Supravalvular Aortic Stenosis. In: Berbari, A., Mancia, G. (eds) Disorders of Blood Pressure Regulation. Updates in Hypertension and Cardiovascular Protection. Springer, Cham. https://doi.org/10.1007/978-3-319-59918-2_15

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  • DOI: https://doi.org/10.1007/978-3-319-59918-2_15

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