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Double-Outlet Right Ventricle

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Congenital Heart Disease in Pediatric and Adult Patients

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Abstract

Anesthetizing a patient with double-outlet right ventricle (DORV) requires an understanding of a large spectrum of anatomic and physiologic variants. Caring for these patients may include preparing for a patient with dynamic right ventricular outflow obstruction similar to tetralogy of Fallot (TOF) or preparing for one with unrestricted pulmonary overcirculation. With an incidence of 3–9/100,000 live births, this lesion is relatively rare, but the physiologic considerations of managing these patients are important to those in settings where they will care for patients with congenital heart disease, both because they will likely encounter these patients and because principle guiding the management of these patients is applicable to many other, such as those with transposition of the great arteries and TOF. Here we review the anatomic and physiologic considerations of managing these patients and frame the chapter with clinical vignettes to highlight anesthetic management goals.

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Authors and Affiliations

  1. Texas Children’s Hospital, Baylor College of Medicine, 6621 Fannin Street, WT-17417, Houston, TX, 77030, USA

    Zoel Augusto Quiñónez MD

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  1. Zoel Augusto Quiñónez MD
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Correspondence to Zoel Augusto Quiñónez MD .

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Editors and Affiliations

  1. Cardiac Anesthesiology Department, Anesthesiology Research Center Shahid Beheshti University of Medical Sciences, Tehran, Iran

    Ali Dabbagh

  2. Kaiser Permanente Los Angeles Medical Center Division of Cardiac Anesthesiology, Los Angeles, California, USA

    Antonio Hernandez Conte

  3. Department of Anesthesiology, Cedars-Sinai Medical Center, Los Angeles, California, USA

    Lorraine Lubin

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Quiñónez, Z.A. (2017). Double-Outlet Right Ventricle. In: Dabbagh, A., Conte, A., Lubin, L. (eds) Congenital Heart Disease in Pediatric and Adult Patients. Springer, Cham. https://doi.org/10.1007/978-3-319-44691-2_27

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  • DOI: https://doi.org/10.1007/978-3-319-44691-2_27

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