Abstract
Congenital heart defects constitute the most common type of birth defects and occur in approximately 8 in 1000 live births. With the exclusion of bicuspid aortic valve disease, the majority of untreated patients born with congenital heart disease (CHD) expire in childhood with approximately 15–25 % surviving into adulthood. Significant advances in prenatal diagnosis, interventional cardiology techniques, congenital heart surgery, anesthesiology, and critical care have allowed approximately 90 % of these patients to survive into adulthood. The profile of patients with congenital heart disease has evolved, and now there are estimates to suggest that in the United States, there are more adults than children living with congenital heart disease. Most of these patients will require additional interventional cardiology or cardiac surgical procedures either palliative or curative during adulthood. Although major studies evaluating this population have not been done, adults with CHD are a medically fragile group, which have an increased risk for perioperative morbidity and mortality. Formal guidelines which direct the management of these patients have not been developed; however, the American College of Cardiology recommends that adult patients with moderate to severe CHD be referred to a center specializing in the care of these patients and receive expert consultation with the appropriate care providers such as adult congenital heart cardiologists, surgeons, and anesthesiologists prior to undergoing procedures.
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Bibliography
Baum VC, Perloff JK. Anesthetic implications of adults with congenital heart disease. Anesth Analg. 1993;76:1342.
Brickner ME, Hillis LD, Lange RA. Congenital heart disease in adults. Part one & two. N Engl J Med. 2000;342:334–42.
Cannesson M, Earing M, Collange V. Anesthesia for noncardiac surgery in adults with congenital heart disease. Anesthesiology. 2009;111(2):432–40.
Hosking MP, Beynen FM. The modified Fontan procedure: physiology and anesthetic implications. J Cardiothorac Vasc Anesth. 1992;6:465–75.
Hucin B, Voriskova M, Hruda J, et al. Late complications and quality of life after atrial correction of transposition of the great arteries in 12 to 18 year follow up. J Cardiovasc Surg. 2000;41:233–9.
Khairy P, Poirier N, Mercier LA. Univentricular heart. Circulation. 2007;115:800–12.
Landzberg MJ, Murphy Jr DJ, Davidson Jr WR, Jarcho JA, Krumholz HM, Mayer Jr JE, Mee RB, Sahn DJ, Van Hare GF, Webb GD. Task force 4: organization of delivery systems for adults with congenital heart disease. J Am Coll Cardiol. 2001;37:1187–93.
Marelli AJ, Mackie AS, et al. Congenital heart disease in the general population: changing prevalence and age distribution. Circulation. 2007;115:163–72.
Perloff JK, Child JS. Congenital heart disease in adults. 3rd ed. Philadelphia: WB Saunders; 2008.
Perloff JK, Warner CA. Challenges posed by adults with repaired congenital heart disease. Circulation. 2001;103:2637–43.
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Lubin, L., Wong, R. (2017). Anesthetic Management of Adults with Congenital Heart Disease. In: Dabbagh, A., Conte, A., Lubin, L. (eds) Congenital Heart Disease in Pediatric and Adult Patients. Springer, Cham. https://doi.org/10.1007/978-3-319-44691-2_13
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DOI: https://doi.org/10.1007/978-3-319-44691-2_13
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