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Catecholaminergic Polymorphic Ventricular Tachycardia

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Clinical Cardiogenetics

Abstract

Catecholaminergic polymorphic ventricular tachycardia is a rare yet severe inherited arrhythmia syndrome characterized by polymorphic ventricular tachyarrhythmias during exercise or emotion. It is caused by mutations in genes involved in intracellular calcium cycling. β-Blockers and lifestyle advices are the cornerstone of therapy.

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Authors and Affiliations

  1. AMC Heart Center, Department of Clinical and Experimental Cardiology, Academic Medical Center, University of Amsterdam, Amsterdam, The Netherlands

    Krystien V. Lieve MD & Christian van der Werf MD, PhD

  2. AP-HP, Hôpital Bichat, Département de Cardiologie et Centre de Référence des Maladies Cardiaques Héréditaires, Université Paris Diderot, Sorbonne Paris Cité, Paris, France

    Antoine Leenhardt MD

Authors
  1. Krystien V. Lieve MD
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  2. Antoine Leenhardt MD
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  3. Christian van der Werf MD, PhD
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Correspondence to Christian van der Werf MD, PhD .

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Editors and Affiliations

  1. Department of Cardiology, St. Elisabeth-TweeSteden Ziekenhuis, Tilburg, The Netherlands

    Hubert F. Baars

  2. Department of Cardiology, University Medical Center Utrecht, Utrecht, The Netherlands

    Pieter A. F. M. Doevendans

  3. Department of Clinical Genetics, VU University Medical Center, Amsterdam, The Netherlands

    Arjan C. Houweling

  4. Department of Clinical Genetics, Academic Medical Center, Amsterdam, The Netherlands

    J. Peter van Tintelen

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Lieve, K.V., Leenhardt, A., van der Werf, C. (2016). Catecholaminergic Polymorphic Ventricular Tachycardia. In: Baars, H., Doevendans, P., Houweling, A., van Tintelen, J. (eds) Clinical Cardiogenetics. Springer, Cham. https://doi.org/10.1007/978-3-319-44203-7_12

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  • DOI: https://doi.org/10.1007/978-3-319-44203-7_12

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