Abstract
Vein of Galen aneurysmal malformations (VGAMs) are rare vascular malformations involving the median prosencephalic vein of Markowski, the precursor of the vein of Galen and the embryonic drainage of the choroid plexus. Although reported to comprise 30 % of pediatric vascular and 1 % of pediatric congenital anomalies [1], the exact incidence of VGAMs is difficult to quantify given the array of vascular pathology causing dilation of the median prosencephalic vein of Markowski or the vein of Galen [2]. In this chapter, we review relevant VGAM vascular anatomy and embryology, classifications schemes, clinical features and pathophysiology, and treatment strategies.
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The authors have no conflicts of interest, sources of financial support, or industry affiliations to disclose relevant to this investigation.
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Stapleton, C.J., Torok, C.M., Koch, M.J., Patel, A.B. (2016). Vein of Galen Aneurysmal Malformations. In: Agrawal, A., Britz, G. (eds) Pediatric Vascular Neurosurgery. Springer, Cham. https://doi.org/10.1007/978-3-319-43636-4_10
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