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Anorectal Malformations

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Pediatric Neurogastroenterology

Abstract

Anorectal malformations (ARM) are a spectrum of congenital abnormalities of the terminal portion of the hindgut which lies partially or completely outside the anal sphincter mechanism. In these conditions, the gastrointestinal tract ends blindly or opens ectopically to the skin or the genitourinary tract (fistula). They affect about 1 in 5000 live births worldwide with a slight male predominance. This chapter is an overview of the clinical aspects of ARM with emphasis on the neonatal and definitive management. Since it is not always possible to correct completely these anomalies, long-term consequences with impacts on quality of life are frequent.

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Authors and Affiliations

  1. Department of Pediatric Surgery, Sainte-Justine University Hospital Center, 3175, cote-Sainte-Catherine, Montreal, QC, Canada, H3T 1C5

    Ann Aspirot M.D.

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  1. Ann Aspirot M.D.
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Correspondence to Ann Aspirot M.D. .

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Editors and Affiliations

  1. Division of Pediatric Gastroenterology Hepatology and Nutrition, CHU Sainte-Justine, Montreal, Québec, Canada

    Christophe Faure

  2. Department of Paediatric Gastroenterology, UCL Institute of Child Health, London, United Kingdom

    Nikhil Thapar

  3. Division of Pediatric Gastroenterology Hepatology, and Nutrition, Nationwide Children’s Hospital, Columbus, Ohio, USA

    Carlo Di Lorenzo

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Aspirot, A. (2017). Anorectal Malformations. In: Faure, C., Thapar, N., Di Lorenzo, C. (eds) Pediatric Neurogastroenterology. Springer, Cham. https://doi.org/10.1007/978-3-319-43268-7_29

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