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Pediatric Neurogastroenterology pp 243–252Cite as

Esophageal Achalasia

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Abstract

Achalasia is the most recognized esophageal primary motor disorder presenting with dysphagia secondary to functional obstruction due to the affection of the body of the esophagus and the lower esophageal sphincter. It is characterized by the absence of peristalsis and incomplete relaxation of the lower esophageal sphincter. An overview of the clinical aspects of this disease is presented with an emphasis on the latest therapeutic advances.

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Authors and Affiliations

  1. Department of Pediatric Surgery, Sainte-Justine University Hospital Center, 3175, Cote-Sainte-Catherine, Montreal, QC, H3T 1C5, Canada

    Ann Aspirot M.D.

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  1. Division of Pediatric Gastroenterology Hepatology and Nutrition, CHU Sainte-Justine, Montreal, Québec, Canada

    Christophe Faure

  2. Department of Paediatric Gastroenterology, UCL Institute of Child Health, London, United Kingdom

    Nikhil Thapar

  3. Division of Pediatric Gastroenterology Hepatology, and Nutrition, Nationwide Children’s Hospital, Columbus, Ohio, USA

    Carlo Di Lorenzo

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Aspirot, A. (2017). Esophageal Achalasia. In: Faure, C., Thapar, N., Di Lorenzo, C. (eds) Pediatric Neurogastroenterology. Springer, Cham. https://doi.org/10.1007/978-3-319-43268-7_21

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