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Choroid Plexus Tumors

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Book cover Adult CNS Radiation Oncology

Abstract

Choroid plexus tumors (CPT) are rare tumors of the neuroepithelial tissue of the brain that are most common in young children. In adults, they arise most frequently in the fourth ventricle, often presenting with hydrocephalus due to overproduction of CSF. There are three histopathological classifications of choroid plexus tumors: choroid plexus papilloma (CPP), atypical choroid plexus papilloma (ACP), and choroid plexus carcinoma (CPC). Histology and extent of surgical resection are prognostic for choroid plexus tumors. Curative treatment for CPP and ACP is typically maximum surgical resection, although recurrence rates are higher in cases of ACP. CPP and ACP have better prognosis than CPC, which often requires multiple modalities for treatment.

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Author information

Authors and Affiliations

  1. Cleveland Clinic Lerner College of Medicine, Cleveland, OH, USA

    Christina Snider

  2. Department of Radiation Oncology, Taussig Cancer Institute, Cleveland Clinic, Cleveland, OH, USA

    John H. Suh & Erin S. Murphy

  3. Rose Ella Burkhardt Brain Tumor and Neuro-oncology Center, Cleveland Clinic, Cleveland, OH, USA

    John H. Suh & Erin S. Murphy

Authors
  1. Christina Snider
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  2. John H. Suh
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  3. Erin S. Murphy
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Corresponding author

Correspondence to Erin S. Murphy .

Editor information

Editors and Affiliations

  1. Department of Radiation Oncology, Keck School of Medicine of USC, Norris Cancer Hospital, Los Angeles, California, USA

    Eric L. Chang

  2. Department of Radiation Oncology, Mayo Clinic, Rochester, Minnesota, USA

    Paul D. Brown

  3. Department of Radiation Oncology, University of Washington Medical Center, Seattle, Washington, USA

    Simon S. Lo

  4. Department of Radiation Oncology, Sunnybrook Health Sciences Centre, University of Toronto, Toronto, Ontario, Canada

    Arjun Sahgal

  5. Department of Radiation Oncology, Taussig Cancer Institute Cleveland Clinic, Cleveland, Ohio, USA

    John H. Suh

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Snider, C., Suh, J.H., Murphy, E.S. (2018). Choroid Plexus Tumors. In: Chang, E., Brown, P., Lo, S., Sahgal, A., Suh, J. (eds) Adult CNS Radiation Oncology. Springer, Cham. https://doi.org/10.1007/978-3-319-42878-9_20

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  • DOI: https://doi.org/10.1007/978-3-319-42878-9_20

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-42877-2

  • Online ISBN: 978-3-319-42878-9

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