Abstract
Is it a sarcoma? Is it a melanoma? Clear cell sarcoma (CCS), also called clear cell sarcoma of tendons and aponeuroses [1, 2], has features of both. CCS represents <1 % of all sarcomas. Since it starts in soft tissue and usually does not affect skin [3], CCS is anatomically distinct from melanoma. Patients are typically younger, between 15 and 45 years of age, and women are more commonly affected than men, though some series indicate equal incidence. The foot and ankle are common primary locations for this rare sarcoma. Age and site distribution for adult patients are shown in Figs. 18.1 and 18.2.
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Brennan, M.F., Antonescu, C.R., Alektiar, K.M., Maki, R.G. (2016). Clear Cell Sarcoma/Melanoma of Soft Parts. In: Management of Soft Tissue Sarcoma. Springer, Cham. https://doi.org/10.1007/978-3-319-41906-0_18
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DOI: https://doi.org/10.1007/978-3-319-41906-0_18
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