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Pathophysiology of IgG4-Related Disease

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Book cover Systemic Fibroinflammatory Disorders

Part of the book series: Rare Diseases of the Immune System ((RDIS))

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Abstract

The concept of IgG4-related disease (IgG4-RD) as a systemic fibroinflammatory disease has been introduced in the very recent past. Many formerly thought “single-organ diseases” are now being summarized as organ manifestations of IgG4-RD. Therefore, much of the literature focusing on the causes of these disorders has been published on certain organ manifestations (e.g., autoimmune pancreatitis) rather than specifically on multisystemic IgG4-RD patients.

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Conflict of Interest Statement

Jochen Zwerina has a received an unrestricted research grant from Roche.

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  1. Ludwig Boltzmann Institute of Osteology at the Hanusch Hospital of WGKK and AUVA Trauma Centre Meidling, 1st Medical Department, Hanusch Hospital, Vienna, Austria

    Jochen Zwerina

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Correspondence to Jochen Zwerina .

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  1. Department of Nephrology, University Hospital, Parma, Italy

    Augusto Vaglio

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Zwerina, J. (2017). Pathophysiology of IgG4-Related Disease. In: Vaglio, A. (eds) Systemic Fibroinflammatory Disorders. Rare Diseases of the Immune System. Springer, Cham. https://doi.org/10.1007/978-3-319-41349-5_5

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  • DOI: https://doi.org/10.1007/978-3-319-41349-5_5

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