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Idiopathic Mediastinal Fibrosis

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Systemic Fibroinflammatory Disorders

Part of the book series: Rare Diseases of the Immune System ((RDIS))

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Abstract

Fibrosing mediastinitis, also known as mediastinal fibrosis or sclerosing mediastinitis, is a clinical entity characterized by abnormal proliferation of fibrous tissue within the mediastinum. The compression of mediastinal vital structures by the fibroinflammatory tissue determines the clinical presentation [1]. Primitive and secondary forms have been described.

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Author information

Authors and Affiliations

  1. Nephrology, University of Parma Medical School, Parma, Italy

    Giovanni M. Rossi

  2. Internal Medicine, Careggi Hospital, Florence, Italy

    Giacomo Emmi

  3. Department of Experimental and Clinical Medicine, University of Firenze, Firenze, Italy

    Giacomo Emmi

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  1. Giovanni M. Rossi
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Correspondence to Giacomo Emmi .

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Editors and Affiliations

  1. Department of Nephrology, University Hospital, Parma, Italy

    Augusto Vaglio

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Rossi, G.M., Emmi, G. (2017). Idiopathic Mediastinal Fibrosis. In: Vaglio, A. (eds) Systemic Fibroinflammatory Disorders. Rare Diseases of the Immune System. Springer, Cham. https://doi.org/10.1007/978-3-319-41349-5_10

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  • DOI: https://doi.org/10.1007/978-3-319-41349-5_10

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-41347-1

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