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Evidence-Based Treatment for Congenital Scoliosis

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Paediatric Orthopaedics
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Abstract

Management of congenital scoliosis begins with the recognition of the patterns of congenital anomalies and the anticipation of the risk of deformity progression. The natural history and prognosis of a patient with congenital scoliosis can vary considerably as illustrated by many of the early descriptive reports. Despite a variety of different surgical strategies that have been described for congenital scoliosis to date, very little evidence exists supporting the most ideal management strategy from timing of intervention to most appropriate surgical technique, to efficacy of the available procedures in altering the natural history of congenital scoliosis. This chapter will outline the available literature, its limitations, and whether evidence-based recommendations can be made around treatment strategies for congenital scoliosis.

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References

  1. Kuhns JG, Hormell RS. Management of congenital scoliosis. Review of one hundred seventy cases. Arch Surg. 1952;65:250–63.

    Article  CAS  Google Scholar 

  2. Winter RB, Moe JH, Eilers VE. Congenital scoliosis: a study of 234 patients treated and untreated. J Bone Joint Surg A. 1968;50:15–47.

    Google Scholar 

  3. McMaster MJ, Ohtsuka K. The natural history of congenital scoliosis. A study of two hundred and fifty-one patients. J Bone Joint Surg A. 1982;64:1128–47.

    Article  CAS  Google Scholar 

  4. McMaster MJ. Congenital scoliosis caused by a unilateral failure of vertebral segmentation with contralateral hemivertebrae. Spine. 1998;23(9):998–1005.

    Article  CAS  PubMed  Google Scholar 

  5. Winter RB, Moe JH, MacEwen D, et al. The Milwaukee brace in the nonoperative treatment of congenital scoliosis. Spine. 1976;1:85–96.

    Article  Google Scholar 

  6. Demirkiran HG, Bekmez S, Celilov R, et al. Serial derotational casting in congenital scoliosis as a time-buying strategy. J Pediatr Orthop. 2015;35(1):43–9.

    Article  PubMed  Google Scholar 

  7. Hedden D. Management themes in congenital scoliosis. J Bone Joint Surg A. 2007;89(suppl 1):72–8.

    Google Scholar 

  8. Goldberg CJ, Moore DP, Fogarty EE, et al. Long-term results from in situ fusion for congenital vertebral deformity. Spine. 2002;27(6):619–28.

    Article  PubMed  Google Scholar 

  9. Vitale MG, Matsumoto H, Bye MR, et al. A retrospective cohort study of pulmonary function, radiographic measures, and quality of life in children with congenital scoliosis: an evaluation of patient outcomes after early spinal fusion. Spine. 2008;33(11):1242–9.

    Article  PubMed  Google Scholar 

  10. Farley FA, Li Y, Jong N, Powell CC, et al. Congenital scoliosis SRS-22 outcomes in children treated with observation, surgery, and VEPTR. Spine. 2014;39(22):1868–74.

    Article  PubMed  Google Scholar 

  11. Karol LA, Johnston C, Mladenov K, et al. Pulmonary function following early thoracic fusion in non-neuromuscular scoliosis. J Bone Joint Surg A. 2008;90:1272–81.

    Article  Google Scholar 

  12. Andrew T, Piggot H. Growth arrest for progressive scoliosis: combined anterior and posterior fusion of the convexity. J Bone Joint Surg Br. 1985;67:193–7.

    CAS  PubMed  Google Scholar 

  13. Uzumcugil A, Cil A, Yazici M, et al. Convex growth arrest in the treatment of congenital spinal deformities: revisited. J Pediatr Orthop. 2004;24:658–66.

    Article  PubMed  Google Scholar 

  14. Winter RB, Lonstein JE, Dennis F. Convex growth arerest for progressive congenital scoliosis due to hemivertebra. J Pediatr Orthop. 1988;8:633–8.

    Article  CAS  PubMed  Google Scholar 

  15. Demirkiran G, Yilmaz G, Kaymaz B, et al. Safety and efficacy of instrumented convex growth arrest in treatment of congenital scoliosis. J Pediatr Orthop. 2014;34(3):275–81.

    Article  PubMed  Google Scholar 

  16. Thompson AG, Marks DS, Sayampanathan SR, et al. Long-term results of combined anterior and posterior convex epiphysiodesis for congenital scoliosis due to hemivertebrae. Spine. 1995;20(12):1380–5.

    Article  CAS  PubMed  Google Scholar 

  17. Marks DS, Sayampanathan SR, Thompson AG, et al. Long-term results of convex epiphysiodesis for congenital scoliosis. Eur Spine J. 1995;4(5):296–301.

    Article  CAS  PubMed  Google Scholar 

  18. Keller PM, Lindseth RE, DeRosa GP. Progressive congenital scoliosis treatment using a transpedicular anterior and posterior convex hemiepiphysiodesis and hemiarthrodesis: a preliminary report. Spine. 1994;19(17):1933–9.

    Article  CAS  PubMed  Google Scholar 

  19. Kieffer J, Dubousset J. Combined anterior and posterior convex epiphysiodesis for progressive congenital scoliosis in children aged < or = 5 years. Eur Spine J. 1994;3:120–5.

    Article  CAS  PubMed  Google Scholar 

  20. Walhout RJ, van Rhijn LW, Pruijs JE. Hemi-epiphysiodesis for unclassified congenital scoliosis: immediate results and mid-term follow-up. Eur Spine J. 2002;11:543–9.

    Article  CAS  PubMed  Google Scholar 

  21. Jalanko T, Rintala R, Puisto V, et al. Hemivertebra resection for congenital scoliosis in young children: comparison of clinical, radiographic, and health-related quality of life outcomes between the anteroposterior and posterolateral approaches. Spine. 2011;36(1):41–9.

    Article  PubMed  Google Scholar 

  22. Bollini G, Docquier PL, Viehweger E, Launay F, Jouve JL. Thoracolumbar hemivertebrae resection by double approach in a single procedure: long-term follow-up. Spine. 2006;31(15):1745–57.

    Article  PubMed  Google Scholar 

  23. Bollini G, Docquier PL, Viehweger E, Launay F, Jouve JL. Lumbar hemivertebra resection. J Bone Joint Surg A. 2006;88(5):1043–52.

    Google Scholar 

  24. Deviren V, Berven S, Smith A, et al. Excision of hemivertebrae in the management of congenital scoliosis involving the thoracic and thoracolumbar spine. J Bone Joint Surg Br. 2001;83(4):496–500.

    Article  CAS  PubMed  Google Scholar 

  25. Crostelli M, Mazza O, Mariani M. Posterior approach lumbar and thoracolumbar hemivertebra resection in congenital scoliosis in children under 10 years of age: results with 3 years mean follow up. Eur Spine J. 2014;23(1):209–15.

    Article  PubMed  Google Scholar 

  26. Chang DG, Kim JH, Ha KY, et al. Posterior hemivertebra resection and short segment fusion with pedicle screw fixation for congenital scoliosis in children younger than 10 years: greater than 7-year follow-up. Spine. 2015;40(8):E484–91.

    Article  PubMed  Google Scholar 

  27. Chang DG, Suk SI, Kim JH, et al. Surgical outcomes by the age at the time of surgery in the treatment of congenital scoliosis in children under age 10 years. Spine J. 2015;15:1783–95.

    Article  PubMed  Google Scholar 

  28. Wang S, Zhang J, Qiu G, et al. Posterior hemivertebra resection with bisegmental fusion for congenital scoliosis: more than 3 year outcomes and analysis of unanticipated surgeries. Eur Spine J. 2013;22(2):387–93.

    Article  PubMed  Google Scholar 

  29. Ruf M, Jensen R, Letko L, et al. Hemivertebra resection and osteotomies in congenital spine deformity. Spine. 2009;34(17):1791–9.

    Article  PubMed  Google Scholar 

  30. Nakamura H, Matsuda H, Konishi S, et al. Single-stage excision of hemivertebrae via the posterior approach alone for congenital scoliosis. Spine. 2002;27(1):110–5.

    Article  PubMed  Google Scholar 

  31. Zhang J, Shengru W, Qui G, et al. The efficacy and complications of posterior hemivertebra resection. Eur Spine J. 2011;20:1692–702.

    Article  PubMed  PubMed Central  Google Scholar 

  32. Yaszay B, O’Brien M, Shufflebarger HL, et al. Efficacy of hemivertebra resection for congenital scoliosis: a multicenter retrospective comparison of three surgical techniques. Spine. 2011;36(24):2052–60.

    Article  PubMed  Google Scholar 

  33. Lee CS, Hwang CJ, Kim DJ, et al. Feasibility of correction with instrumentation only in congenital scoliosis. Neurosurgery. 2014;74(1):35–41.

    Article  PubMed  Google Scholar 

  34. Goldberg CJ, Gillic I, Connaughton O, et al. Respiratory function and cosmesis at maturity in infantile-onset scoliosis. Spine. 2003;28:2397–406.

    Article  CAS  PubMed  Google Scholar 

  35. Kose N, Campbell Jr RM. Congenital scoliosis. Med Sci Monit. 2004;10(5):RA104–10.

    PubMed  Google Scholar 

  36. Campbell RM, Smith MD, Mayes TE, et al. The characteristics of thoracic insufficiency syndrome associated with fused ribs and congenital scoliosis. J Bone Joint Surg A. 2003;85:399–408.

    Article  Google Scholar 

  37. Hell AK, Campbell RM, Hefti F. The vertical expandable prosthetic titanium rib implant for the treatment of thoracic insufficiency syndrome associated with congenital and neuromuscular scoliosis in young children. J Pediatr Orthop B. 2005;14(4):287–93.

    Article  PubMed  Google Scholar 

  38. Flynn JM, Emans JB, Smith JT, et al. VEPTR to treat nonsyndromic congenital scoliosis: a multicenter, mid-term follow-up study. J Pediatr Orthop. 2013;33(7):679–84.

    Article  PubMed  Google Scholar 

  39. Elsebai HB, Yazici M, Thompson GH, et al. Safety and efficacy of growing rod technique for pediatric congenital spinal deformities. J Pediatr Orthop. 2011;31(1):1–5.

    Article  PubMed  Google Scholar 

  40. Wang S, Zhang J, Qiu G, et al. Dual growing rods technique for congenital scoliosis: more than 2 years outcomes: preliminary results of a single center. Spine. 2012;37(26):E1639–44.

    Article  PubMed  Google Scholar 

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Correspondence to Firoz Miyanji .

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Miyanji, F. (2017). Evidence-Based Treatment for Congenital Scoliosis. In: Alshryda, S., Huntley, J., Banaszkiewicz, P. (eds) Paediatric Orthopaedics. Springer, Cham. https://doi.org/10.1007/978-3-319-41142-2_25

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  • DOI: https://doi.org/10.1007/978-3-319-41142-2_25

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-41140-8

  • Online ISBN: 978-3-319-41142-2

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