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Pulmonary Valvuloplasty: Fetal, Neonatal, and Follow-Up Outcomes

  • Eva Grohmann
  • Andreas Tulzer
  • Wolfgang Arzt
  • Gerald TulzerEmail author
Chapter

Abstract

The primary management and outcome of unborn children with atresia (PA/IVS) or critical stenosis of the pulmonary valve (CPS) and intact ventricular septum are still under discussion. The degree of the morphological and clinical picture of this disease can vary from a hypoplastic right heart syndrome with a univentricular physiology to a biventricular heart only with the need for valvuloplasty after delivery. Neonates with CPS or PA/IVS show considerable variation of abnormalities of the right ventricle, tricuspid valve (TV), and coronary arteries. Therefore, there is a wide range in the reported 5-year survival rate from 50 to 86% [1]. This cardiac malformation is rarely associated with chromosomal defects or extra-cardiac malformations. Therefore, the cardiologist’s prediction of a univentricular or biventricular circulation could have even more influence on the parents’ choice regarding the future of the pregnancy [2]. The focus of this chapter lies especially on the fetal and neonatal outcome of fetuses, who underwent pulmonary valvuloplasty in utero.

Keywords

Tricuspid Valve Pericardial Effusion Pulmonary Valve Intact Ventricular Septum Biventricular Circulation 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

References

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    Tworetzky W, McElhinney DB, Marx GR, Benson CB, Brusseau R, Morash D, et al. In utero valvuloplasty for pulmonary atresia with hypoplastic right ventricle: techniques and outcomes. Pediatrics. 2009;124(3):e510–8.CrossRefPubMedPubMedCentralGoogle Scholar

Copyright information

© Springer International Publishing Switzerland 2016

Authors and Affiliations

  • Eva Grohmann
    • 1
  • Andreas Tulzer
    • 1
  • Wolfgang Arzt
    • 2
  • Gerald Tulzer
    • 1
    Email author
  1. 1.Department of Pediatric CardiologyChildren’s Heart Center Linz, Kepler University Hospital LinzLinzAustria
  2. 2.Institute of Prenatal MedicineKepler University Hospital LinzLinzAustria

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