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Prognosis, Clinical Course, and Monitoring of Patients with Idiopathic Pulmonary Fibrosis

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Guide to Clinical Management of Idiopathic Pulmonary Fibrosis

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Abstract

The prognosis of idiopathic pulmonary fibrosis (IPF) is generally regarded as quite poor with a median survival from the time of diagnosis of anywhere from 2.5 to 4 years [1]. However, it is difficult a priori to predict the course of the disease in individual patients [2]. There are some patients who have a protracted course and survive 5 years or more, but this disease phenotype can only be recognized in retrospect. This represents about 20–25 % of all patients with IPF [3].

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Authors and Affiliations

  1. Inova Fairfax Medical Campus, Falls Church, Virginia, USA

    Steven D Nathan, A Whitney Brown & Christopher S King

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  1. Steven D Nathan
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  2. A Whitney Brown
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  3. Christopher S King
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Nathan, S.D., Brown, A.W., King, C.S. (2016). Prognosis, Clinical Course, and Monitoring of Patients with Idiopathic Pulmonary Fibrosis. In: Guide to Clinical Management of Idiopathic Pulmonary Fibrosis. Adis, Cham. https://doi.org/10.1007/978-3-319-32794-5_5

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  • DOI: https://doi.org/10.1007/978-3-319-32794-5_5

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  • Publisher Name: Adis, Cham

  • Print ISBN: 978-3-319-32792-1

  • Online ISBN: 978-3-319-32794-5

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