Childhood vasculitis includes a challenging group of conditions that often require multi-specialty care by dermatology, rheumatology, nephrology, cardiology, neurology, gastroenterology, and general pediatrics. Vasculitis in children may be from infection, autoimmune disorders, drug induced, related to malignancy, or idiopathic. A skin biopsy is essential for the diagnosis of many types of vasculitis. The most common type of childhood vasculitis is Henoch–Schönlein Purpura. This chapter discusses several types of pediatric vasculitis including Henoch–Schönlein Purpura, Polyarteritis nodosa, and Acute Hemorrhagic Edema of Infancy.
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