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Choroid Plexus Tumors

  • Nalin GuptaEmail author
Chapter
Part of the Pediatric Oncology book series (PEDIATRICO)

Abstract

The choroid plexus has the highly specialized function of producing cerebrospinal fluid (CSF). It is anatomically localized to the parenchymal/ventricular junction in all four ventricles. The choroid plexus itself is derived from the ventricular epithelium along certain segments of the neural tube, and there is a common ontogeny between choroid epithelium and cells of glial origin which can lead to diagnostic confusion. Tumors arising from the choroid plexus can display a benign or malignant phenotype, but conversion to a malignant phenotype is a rare event. Surgical resection of benign choroid plexus papillomas is often curative while choroid plexus carcinomas require adjuvant therapy and recurrence is common.

Keywords

Choroid Plexus Gross Total Resection Choroid Plexus Papilloma Malignant Rhabdoid Tumor Choroid Plexus Carcinoma 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer International Publishing 2017

Authors and Affiliations

  1. 1.Division of Pediatric Neurosurgery, Departments of Neurological Surgery and PediatricsUniversity of California San Francisco & UCSF Benioff Children’s HospitalSan FranciscoUSA

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