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Nonmalignant Hematology pp 243–254Cite as

Congenital Disorders of Fibrinogen: Clinical Presentations, Diagnosis and Management

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Abstract

Congenital fibrinogen disorders (CFD) include two subtypes of fibrinogen defects: quantitative disorders, defined by absent (afibrinogenaemia) or decreased (hypofibrinogenaemia) fibrinogen levels, and qualitative disorders characterised by a discrepancy between functional and antigenic values of fibrinogen (dysfibrinogenaemia and hypodysfibrinogenaemia) (de Moerloose et al. 2013).

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Authors and Affiliations

  1. Angiology and Haemostasis Division, University Hospitals and Faculty of Medicine of Geneva, 4, Rue Gabrielle-Perret-Gentil, Geneva, 1205, Switzerland

    Alessandro Casini & Philippe de Moerloose

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  1. Alessandro Casini
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  2. Philippe de Moerloose
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Correspondence to Alessandro Casini .

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Editors and Affiliations

  1. Cancer Treatment Centers of America, Department of Hematology and Bone Marrow Transplantion, Zion, Illinois, USA

    Syed A. Abutalib

  2. Dana-Farber Cancer Institute, Brigham and Women's Hospital, Boston, Massachusetts, USA

    Jean M. Connors

  3. Department of Medicine, University of Pittsburgh Medical Center, Pittsburgh, Pennsylvania, USA

    Margaret V. Ragni

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Casini, A., de Moerloose, P. (2016). Congenital Disorders of Fibrinogen: Clinical Presentations, Diagnosis and Management. In: Abutalib, S., Connors, J., Ragni, M. (eds) Nonmalignant Hematology. Springer, Cham. https://doi.org/10.1007/978-3-319-30352-9_22

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