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Rare Genitourinary Tumors pp 361–367Cite as

Rare Tumors of the Vulva

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Abstract

Vulvar cancer is an uncommon malignancy with approximately 5,000 new cases and 1,100 related deaths per year in the United States. The majority of cases are squamous cell carcinoma, but approximately 10 % are less common histologic types including melanoma, basal cell carcinoma, sarcoma, Bartholin’s gland carcinoma, verrucous carcinoma, and Paget’s disease of the vulva. This chapter reviews the epidemiology, presenting symptoms, treatment, and prognosis for each of these rare, non-squamous cell vulvar tumors. Because there are limited studies describing these uncommon entities, the recommended treatment is often similar to the more common squamous cell carcinoma of the vulva. Additional research is needed to determine the optimal management for these rare vulvar malignancies.

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Author information

Authors and Affiliations

  1. The Department of Obstetrics and Gynecology, Federal University of Health Sciences Porto Alegre (UFCSPA)/Irmandade Santa Casa de Misericordia de Porto Alegre, Porto Alegre, Brazil

    Mila Pontremoli Salcedo

  2. Division of Gynecologic Oncology, Vincent Obstetrics and Gynecology, Massachusetts General Hospital, Harvard Medical School, Boston, MA, USA

    Marcela G. del Carmen MD

  3. Department of Gynecologic Oncology and Reproductive Medicine, The University of Texas MD Anderson Cancer Center, 1515 Holcombe Blvd., Houston, TX, 77030, USA

    Kathleen M. Schmeler MD

Authors
  1. Mila Pontremoli Salcedo
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  2. Marcela G. del Carmen MD
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  3. Kathleen M. Schmeler MD
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Corresponding author

Correspondence to Kathleen M. Schmeler MD .

Editor information

Editors and Affiliations

  1. Department of Oncology, Mayo Clinic, Division of Medical Oncology, Rochester, Minnesota, USA

    Lance Pagliaro

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© 2016 Springer International Publishing Switzerland

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Salcedo, M.P., del Carmen, M.G., Schmeler, K.M. (2016). Rare Tumors of the Vulva. In: Pagliaro, L. (eds) Rare Genitourinary Tumors. Springer, Cham. https://doi.org/10.1007/978-3-319-30046-7_23

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  • DOI: https://doi.org/10.1007/978-3-319-30046-7_23

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-30044-3

  • Online ISBN: 978-3-319-30046-7

  • eBook Packages: MedicineMedicine (R0)

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