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Biliary Atresia

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Fundamentals of Pediatric Surgery

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Abstract

Biliary atresia is a serious condition affecting bile drainage from the liver to the small intestine caused by a progressive fibro-proliferative obliteration of the extrahepatic bile ducts. Untreated, it can lead to progressive liver failure, cirrhosis, and death. Broadly two types of biliary atresia exist, acquired and fetal. Infants with persistent jaundice or acholic stools beyond 3 weeks of life should be evaluated for biliary atresia. Definitive treatment requires Kasai portoenterostomy or liver transplantation. Biliary atresia requires a methodical and multidisciplinary diagnostic workup and treatment plan.

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Author information

Authors and Affiliations

  1. Department of General Surgery, Children’s Hospital of Philadelphia, 34th St. and Civic Center Blvd., Philadelphia, PA, 19104, USA

    Joseph B. Lillegard MD, PhD

  2. Department of Surgery, Hospital of the University of Pennsylvania, 3400 Spruce Street, Philadelphia, PA, 19104, USA

    Avery C. Miller MD

  3. Department of General Surgery, Children’s Hospital of Philadelphia, 34th and Civic Center Blvd., Philadelphia, PA, 19104, USA

    Alan W. Flake MD

Authors
  1. Joseph B. Lillegard MD, PhD
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  2. Avery C. Miller MD
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  3. Alan W. Flake MD
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Corresponding author

Correspondence to Alan W. Flake MD .

Editor information

Editors and Affiliations

  1. Department of General Surgery, The Children’s Hospital of Philadelphia, Philadelphia, Pennsylvania, USA

    Peter Mattei

  2. Division of Pediatric Surgery Department of Surgery, University of Wisconsin, Madison, Wisconsin, USA

    Peter F. Nichol

  3. Primary Children’s Hospital Department of Surgery, University of Utah, Salt Lake City, Utah, USA

    Michael D. Rollins, II

  4. Departments of Surgery and Pediatrics, Alpert Medical School of Brown University, Providence, Rhode Island, USA

    Christopher S. Muratore

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© 2017 Springer International Publishing AG

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Lillegard, J.B., Miller, A.C., Flake, A.W. (2017). Biliary Atresia. In: Mattei, P., Nichol, P., Rollins, II, M., Muratore, C. (eds) Fundamentals of Pediatric Surgery. Springer, Cham. https://doi.org/10.1007/978-3-319-27443-0_78

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  • DOI: https://doi.org/10.1007/978-3-319-27443-0_78

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-27441-6

  • Online ISBN: 978-3-319-27443-0

  • eBook Packages: MedicineMedicine (R0)

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