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Tetralogy of Fallot with Complete Atrioventricular Canal

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Surgery of Conotruncal Anomalies

Abstract

Tetralogy of Fallot associated with complete atrioventricular canal (TC) is a relatively rare form of conotruncal anomaly. The indications for a systemico-pulmonary shunt are few today. We favor a two patch technique. Most of the time, the VSD patch closure is performed through the right atrium only; however a ventriculotomy is used when needed.

The early mortality is contemporarily between 0 and 10 %. Risk factors for morbidity and mortality include: persistent or residual left AVV insufficiency, residual shunting at the ventricular level, residual RVOT obstruction particularly in association with TV regurgitation, and LVOT obstruction. Long-term actuarial survival in recent series show: 86 % survival at 1-year, 82 % at 5 years, 77 % at 7 years, and 72 % at 15 years.

Modern management of patients with Tetralogy of Fallot and Complete AVSD has proven that surgical intervention does not confer mortality, morbidity, or long-term functional status significantly outside the range of what could be expected for isolated TOF or CAVC patients.

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Authors and Affiliations

  1. Division of Cardiothoracic Surgery, Department of Cardiothoracic Surgery, The Children’s Hospital of Philadelphia, 34th Street and Civic Center Blvd., Suite 8527, Philadelphia, PA, 19104, USA

    Thomas L. Spray MD & Michael Lewis MD

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  1. Thomas L. Spray MD
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  2. Michael Lewis MD
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Correspondence to Thomas L. Spray MD .

Editor information

Editors and Affiliations

  1. Royal Brompton Hospital, London, United Kingdom

    Francois Lacour-Gayet

  2. C.S. Mott Children’s Hospital, University of Michigan, Ann Arbor, Michigan, USA

    Edward L. Bove

  3. German Pediatric Heart Center, Asklepios Klinik Sankt Augustin Gmb, Sankt Augustin, Germany

    Viktor Hraška

  4. University of Pittsburgh Medical School, Pittsburgh, Pennsylvania, USA

    Victor O. Morell

  5. Department of Cardiothoracic Surgery, Children’s Hospital of Philadelphia, Philadelphia, Pennsylvania, USA

    Thomas L. Spray

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Spray, T.L., Lewis, M. (2016). Tetralogy of Fallot with Complete Atrioventricular Canal. In: Lacour-Gayet, F., Bove, E., Hraška, V., Morell, V., Spray, T. (eds) Surgery of Conotruncal Anomalies. Springer, Cham. https://doi.org/10.1007/978-3-319-23057-3_9

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  • DOI: https://doi.org/10.1007/978-3-319-23057-3_9

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-23056-6

  • Online ISBN: 978-3-319-23057-3

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