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Bi-ventricular Repair of Double Outlet Right Ventricle

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Book cover Surgery of Conotruncal Anomalies

Abstract

Double outlet right ventricle (DORV) is a type of ventriculo-arterial connection where the great vessels arise entirely or predominantly from the right ventricle. The name DORV encloses a vast spectrum of congenital heart diseases with various clinical presentations and surgical treatment. Rarely a congenital heart disease has been the source of such controversial exchanges around the anatomical definitions and the optimal surgical techniques. The recent Functional Classification has greatly simplified the management of DORV in describing different functional types unified by a common clinical presentation and more importantly by a similar surgical management. The surgical repair of DORV-VSD type, DORV-Fallot and DORV-TGA (Taussig-Bing) is today performed with very low mortality. The surgical anatomy and the optimal surgical technique of DORV non-committed VSD and DORV-AVSD-Heterotaxy are still controversial. In presence of two viable ventricles, we believe that biventricular repair is the optimal solution. This chapter and Chaps. 15 and 24 describe in details biventricular repair of DORV.

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Authors and Affiliations

  1. Department of Pediatric Cardiac Surgery, National Heart and Lung Institute, Royal Brompton Hospital, Imperial College University, Sydney Street, London, SW3 6NP, UK

    Francois Lacour-Gayet MD

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  1. Francois Lacour-Gayet MD
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Correspondence to Francois Lacour-Gayet MD .

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Editors and Affiliations

  1. Royal Brompton Hospital, London, United Kingdom

    Francois Lacour-Gayet

  2. C.S. Mott Children’s Hospital, University of Michigan, Ann Arbor, Michigan, USA

    Edward L. Bove

  3. German Pediatric Heart Center, Asklepios Klinik Sankt Augustin Gmb, Sankt Augustin, Germany

    Viktor Hraška

  4. University of Pittsburgh Medical School, Pittsburgh, Pennsylvania, USA

    Victor O. Morell

  5. Department of Cardiothoracic Surgery, Children’s Hospital of Philadelphia, Philadelphia, Pennsylvania, USA

    Thomas L. Spray

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Lacour-Gayet, F. (2016). Bi-ventricular Repair of Double Outlet Right Ventricle. In: Lacour-Gayet, F., Bove, E., Hraška, V., Morell, V., Spray, T. (eds) Surgery of Conotruncal Anomalies. Springer, Cham. https://doi.org/10.1007/978-3-319-23057-3_23

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  • DOI: https://doi.org/10.1007/978-3-319-23057-3_23

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-23056-6

  • Online ISBN: 978-3-319-23057-3

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